Tratamento ortodôntico-cirúrgico da Síndrome de Crouzon em paciente adulto: relato de caso clínico

Augusto Pary, Julio Pedra e Cal Neto

The Crouzon Syndrome is considered the most common inherited craniofacial synostosis. The condition is characterized by early closure of craniofacial sutures, resulting in deformities affecting the skull and midface. Treatment usually needs several surgical interventions initiating in the first year of life and finishing at 17-18 years old, when the facial growth is completed. However, the expression of the condition is extremely variable and therefore, several patients does not have so severe clinical manifestations to undergo surgery during infancy. Regardless of the severity, currently, the surgical intervention considered as the standard for midface hipoplasia correction is the Le Fort III osteotomy. However, the osteotomy design may need adaptations regarding the clinical presentation of the patient. In this article, an orthodontic-surgical treatment of an adult, treatment-naive patient carrying Crouzon Syndrome is reported. The traditional Le Fort III was modified to not include the nasal region and it was combined to a Le Fort I osteotomy for the midfacial hypoplasia correction. Mandibular osteotomies were also performed to the total correction of the facial deformity. The decisions regarding the orthodontic-surgical planning will be discussed and the surgical technique of the modified Le Fort III osteotomy, described.

Keywords: Craniofacial dysostosis. Osteotomy, Le Fort. Maxillary osteotomy. Osteotomy. Craniosynostoses.

How to cite: Pary A, Pedra e Cal Neto J. Tratamento ortodôntico-cirúrgico da Síndrome de Crouzon em paciente adulto: relato de caso clínico. Rev Clín Ortod Dental Press. 2018 Abr-Maio;17(2):43-54. DOI: https://doi.org/10.14436/1676-6849.17.2.043-054.art

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